Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor in the Adrenal Gland of a Child

Authors

  • Kourosh Goudarzipour Pediatric Congenital Hematologic Disorders Research Center, Shahid Beheshti University of Medical Science, Tehran, Iran Author
  • Farzaneh Farahmandi Mofid Childrens’ Hospital, Shahid Beheshti University of Medical Science, Tehran, Iran Author
  • Ahmad Mohammadi Pediatric Congenital Hematologic Disorders Research Center, Shahid Beheshti University of Medical Science, Tehran, Iran Author
  • Reza Taherian Student Research Committee, School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran Author

Abstract

Ewing sarcoma/peripheral primitive neuroectodermal tumor (ES/PNET) typically occurs in long or flat bones, soft tissues, or less often, solid organs. Ewing sarcoma/peripheral primitive neuroectodermal tumor arising from the adrenal gland is extremely rare, especially in children, and only limited cases are reported previously. Herein, we review a case of a 22-month-old girl who presented to our department with abdominal pain, bulging of the left flank, and a nonfunctioning adrenal lesion which was found to be an adrenal ES/PNET. The patient was successfully treated with surgery and adjuvant chemotherapy. Since delayed diagnosis may result in metastatic lesions, this case underscores the importance of considering ES/PNET in the differential diagnosis of large adrenal masses.

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Published

2018-06-07

Issue

Section

CASE REPORT | Kidney Diseases

How to Cite

Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor in the Adrenal Gland of a Child. (2018). Iranian Journal of Kidney Diseases, 12(3), 190-192. https://ijkd.org/index.php/ijkd/article/view/3667